Biliary atresia (jaundice with pale stools in a baby)

Overview

Bile ducts in a newborn's liver become blocked, so bile can't drain.

Surgery (Kasai procedure) works best before 2 months of age.

Symptoms

Common signs:

• Jaundice past 2 weeks
• Pale, greasy, or floating stools

Less common

• Pale stools
• Dark urine
• Swollen belly

Look up a symptom: Yellow skin or eyes

When to get medical care

Causes

Unknown.

Does it spread or run in families?

• It isn't contagious. You can't catch it from someone else.

Diagnosis

A clinician asks about your symptoms and may order tests.

The exam

A physical exam.

Tests

Tests, if needed:

• Ultrasound:
• Blood tests:

Treatment

Treatment depends on the cause and how severe it is.

Self-care

• Check stool color
• Compare your baby's stool to a stool color card
• Report pale, white, or gray stools

Which doctor treats this

• Start with your child's pediatrician.
• They may send you to a pediatric specialist: a gastroenterologist (stomach and gut doctor) or a surgeon.

Living with it

Support groups and helplines

• Genetic and Rare Diseases Information Center (GARD): Free NIH information on rare diseases, including where to find experts and patient groups.
• National Organization for Rare Disorders (NORD): Patient groups, help finding care, and aid programs for rare diseases.

Children, pregnancy, and older adults

• Babies with jaundice past 2 weeks: Need a check.

For caregivers

• Learn the warning signs and when to call the doctor or 911.
• Keep a list of your child's medicines, doses, and doctors on your phone.
• Tell teachers, coaches, and sitters what to watch for and what to do.
• Take breaks and ask for help. Caregivers need care too.

Outlook

Early surgery helps; some need a transplant later.

Getting ready for your visit

Bring a list of your symptoms and medicines.

What to bring

• A list of your medicines and supplements
• Notes on when symptoms started and what makes them better or worse

Questions to ask

• What's causing this?
• What treatment do you recommend?

Research studies

Research studies test new ways to find and treat health problems. Some are looking for volunteers. Talk with your doctor before joining one.

Search ClinicalTrials.gov for studies on Biliary atresia (jaundice with pale stools in a baby)